transmedТрансляционная медицинаTranslational Medicine2311-44952410-5155Almazov National Medical Research Centre, Saint Petersburg, Russia10.18705/2311-4495-2020-7-5-53-61transmed-579Research ArticleЭНДОКРИНОЛОГИЧЕСКИЕ ЗАБОЛЕВАНИЯMETABOLIC DISEASESПатоморфология атипичной формы врожденного гиперинсулинизма на примере трех клинических случаевPathomorphology of the atypical form of congenital hyperinsulinism on the example of three clinical caseshttps://orcid.org/0000-0002-1946-0029ПерминоваА. А.PerminovaA. A.

Перминова Анастасия Аркадьевна, аспирант 1-го года, патологоанатомическое отделение

ул. Аккуратова, д. 2, Санкт-Петербург, 197341

Perminova Anastasia A., 1st year Postgraduate Student, Pathology Department

Akkuratova str. 2, Saint Petersburg, 197341

aaperminova@yandex.ruhttps://orcid.org/0000-0003-0735-7822МитрофановаЛ. Б.MitrofanovaL. B.

Митрофанова Любовь Борисовна, д.м.н., главный научный сотрудник НИЛ патоморфологии, профессор кафедры патологии Института медицинского образования

Санкт-Петербург

Mitrofanova Lubov B., MD, Dr. Sc., Chief Researcher of the Scientific Research Laboratory of Pathomorphology, Professor of the Department of Pathology

Saint Petersburg

Mitrofanova_LB@almazovcentre.ruhttps://orcid.org/0000-0002-8446-830XБаировВ. Г.BairovV. G.

Баиров Владимир Гиреевич, д.м.н., профессор, главный научный сотрудник НИЛ хирургии врожденной и наследственной патологии Института перинатологии и педиатрии, профессор кафедры хирургических болезней Института медицинского образования

Санкт-Петербург

Bairov Vladimir G., MD, Dr. Sc., Chief Researcher of the Scientific Research Laboratory of Surgery in Congenital and Genetic Diseases, Professor of the Department of Surgery

Saint Petersburg

Bairov_VG@almazovcentre.ruhttps://orcid.org/0000-0002-8734-2227СухоцкаяА. А.SukhotskayaA. A.

Сухоцкая Анна Андреевна, к.м.н., доцент, заведующий отделением детской хирургии пороков развития, Институт перинатологии и педиатрии

Санкт-Петербург

Sukhotskaya Anna A., PhD, Associate Professor, Head of Pediatric Surgery Department

Saint Petersburg

Sukhotskaya_AA@almazovcentre.ruhttps://orcid.org/0000-0002-7086-9153РыжковаД. В.RyzhkovaD. V.

Рыжкова Дарья Викторовна, профессор РАН, д.м.н., главный научный сотрудник научно-исследовательского отдела ядерной медицины и тераностики Института онкологии и гематологии, руководитель научно-клинического объединения ядерной медицины, заведующий кафедрой ядерной медицины и радиационных технологий Института медицинского образования

Санкт-Петербург

Ryzhkova Daria Viktorovna, MD, Dr. Sc., Professor, Head of the Research And Clinical Unit for Nuclear Medicine, Chief Researcher at the nuclear Cardiology Research Laboratory

Saint Petersburg

Ryzhkova_dv@almazovcentre.ruФедеральное государственное бюджетное учреждение «Национальный медицинский исследовательский центр имени В. А. Алмазова» Министерства здравоохранения Российской ФедерацииРоссияAlmazov National Medical Research CentreRussian Federation202012102020755361Copyright © Перминова А.А., Митрофанова Л.Б., Баиров В.Г., Сухоцкая А.А., Рыжкова Д.В., 20202020Перминова А.А., Митрофанова Л.Б., Баиров В.Г., Сухоцкая А.А., Рыжкова Д.В.Perminova A.A., Mitrofanova L.B., Bairov V.G., Sukhotskaya A.A., Ryzhkova D.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://transmed.almazovcentre.ru/jour/article/view/579атипичная форма врожденного гиперинсулинизмаврожденный гиперинсулинизмгипертрофия ядер эндокриноцитовиммуногистохимическое исследованиесоматостатинхромо гранин АIsl1NeuroD1Nkx2.2atypical form of congenital hyperinsulinismchromogranin Acongenital hyperinsulinismhypertrophy of endocrinocyte nucleiimmunohistochemical studyIsl1NeuroD1Nkx2.2somatostatinReferencesMenni F, de Lonlay P, Sevin C, et al. 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The authors declare that there are no conflicts of interest present.